| Table 3: Vasculitis in CF |
|
|
Site
|
No
of cases
|
Diagnosis
|
Treatment
|
Outcome
|
|
Cutaneous
(6, 7, 9, 10, 23, 27, 36, 42)
|
40
(14F, 18M)*
|
Skin
Biopsy, Clinical Suspicion
|
Supportive
Measures Antihistamines NSAIDs Rarely Corticosteroids
|
In
the Majority of Cases Spontaneous Resolution was Reported24 Patients were
Reported Dead within a Few Months from having Purpuric Rash
|
|
GI
(23, 37, 38)
|
4
(3M)*
|
Endoscopy
|
Corticosteroids
|
1
Responded to Corticosteroids3 Diagnosed on Post mortem Examination
|
|
CNS
(6)
|
1
(M)
|
Post-mortem
|
Corticosteroids
|
Fatal
Outcome
|
|
Renal
(6, 9)
|
2
(1M)*
|
Renal
biopsy
|
Corticosteroids
|
Full
Recovery with Treatment
|
Abbreviations:
= F = Female, M = Male. NSAIDs = non-steroidal antiinflammatory drugs * = patients'
gender reported only in a proportion of cases
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